Congenital anomalies that involve the distal segment of urogenital sinus (giving rise to female urethra and vagina) may lead to abnormal urethral development ranging from absent to markedly deficient urethra.
The abnormal division may also cause a short and patulous urethra. Sphincteric defects are likely to be associated and when combined with the short urethral length is a cause for severe urinary incontinence. Urinary incontinence due to a congenital cause requiring repeated urethral reconstruction to relieve symptoms is presented. A 15 year old girl was referred for bothersome urinary incontinence due to a short, wide, patulous urethra with defective sphincteric mechanism as part of urogenital sinus developmental anomaly. She was initially managed by reconstruction of bladder neck and proximal urethra with sphincter augmentation using autologous pubovaginal sling. Persistent urinary incontinence demanded a second urethral reconstruction using tubularised anterior bladder flap (modified Tanagho). Surgical reconstruction of the urethra achieved socially acceptable continence.
Written by:
Rajamaheswari N, Agarwal S, Chhikara AB, Seethalakshmi K. Are you the author?
Department of Urogynaecology, Government Kasturba Gandhi Hospital and Institute of Social Obstetrics, Madras Medical College, Triplicane, Chennai, Tamil Nadu, India.
Reference: Urol Ann. 2013 Jul;5(3):215-7.
doi: 10.4103/0974-7796.115745
PubMed Abstract
PMID: 24049391
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